Intra-Peritoneal Leiomyoma of the Round Ligament in a Patient with Mayer- Rokitansky-Kuster-Hauser (MRKH) Syndrome
نویسنده
چکیده
Background: The occurrence of an extra-uterine leiomyoma, arising from the intra-peritoneal portion of the round ligament in a lady with Müllerian agenesis diagnosed at the age of forty is extremely rare. We report a case of this rare combination in a Middle Eastern woman. Case: A 40 years old lady, primarily amenorrheic, presented to our clinic for an infertility consultation. The work-up showed features suggestive of Mayer-RokitanskyKüster-Hauser (MRKH) syndrome with a leiomyoma arising from the intra-peritoneal part of the round ligament.
منابع مشابه
Intra-peritoneal leiomyoma of the round ligament in a patient with Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome
BACKGROUND The occurrence of an extra-uterine leiomyoma, arising from the intra-peritoneal portion of the round ligament in a lady with Müllerian agenesis diagnosed at the age of forty is extremely rare. We report a case of this rare combination in a Middle Eastern woman. CASE A 40 years old lady, primarily amenorrheic, presented to our clinic for an infertility consultation. The work- up sho...
متن کاملP-192: The Study of Cystic Fibrosis Transmembrane Conductance Regulator Gene Mutations and Polymorphisms in Iranian Patients with Mayer Rokitansky Kuster Hauser Syndrome
Background: Mayer - Rokitansky - Kuster - Hauser (MRKH) syndrome is characterized by congenital aplasia of the uterus and the upper part of the vagina in women showing normal development of secondary sexual characteristics and a normal 46, XX karyotype. Congenital anomaly of the female genital tract, estimated to occur in approximately 1 in every 5,000 females. It is caused by a failure of deve...
متن کاملLarge leiomyoma in a woman with Mayer-Rokitansky-Kuster-Hauser syndrome.
Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a rare congenital anomaly characterized as aplasia or hypoplasia of uterus and vagina in women with normal development of secondary sex characteristics. It affects 1 in 4000-5000 female births. Women with this syndrome present with primary amenorrhoea. MRKH syndrome may be associated with renal, skeletal, cardiac and auditory anomalies. Women wi...
متن کامل[Acute abdomen in a patient with Mayer-Rokitansky-Kuster-Hauser syndrome].
BACKGROUND Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a malformation of female genital tract (incidence 1 in 4000 female newborn children). It appears as a result of a disorder in the development of Millerian cannals. Etiology is unknown. Syndrome MRKH is the most frequent cause of primary amenorrhoea (90%). Patients with MRKH have a normal female phenotype, with normal pubic hairness an...
متن کاملSuccessful Surgical Treatment for Vaginal Agenesis: Report of Two Cases of Mayer–Rokitansky–Küster–Hauser (MRKH) Syndrome
Introduction: Mayer–Rokitansky–Küster–Hauser (MRKH) syndrome is a rare disorder in women which identified as agenesis of vagina and hypoplasia or agenesis of uterine. Case presentation: in this study, two female cases (17, and 19 years old) diagnosed with MRKH (first one type 2, and second one type 1) are described. Both patients were presented with amenorrhea, and absence of vagina orifice. On...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
دوره شماره
صفحات -
تاریخ انتشار 2017